TheraRadar
Data updated: May 26, 2026

EXONDYS 51 (eteplirsen)

Trial Activity: Declining 1 active trials
Orphan Drug Priority Review Accelerated Approval Fast Track
Rare Disease Approved 2016-09-19

EXONDYS 51 is indicated for the treatment of Duchenne Muscular Dystrophy.

Source: FDA Label • Sarepta Therapeutics • Antisense Oligonucleotide

How EXONDYS 51 Works

Eteplirsen is designed to bind to exon 51 of dystrophin pre-mRNA, resulting in the exclusion of this exon during mRNA processing. This mechanism, known as exon skipping, is intended for patients with specific genetic mutations amenable to this process. By skipping exon 51, the drug allows for the production of an internally truncated dystrophin protein.

Development Insights

Sarepta Therapeutics, Inc. conducting 6 trials (86%)
3 indications explored (Focused)
duchenne muscular dystrophy (3 trials)
muscular dystrophy, duchenne (2 trials)
duchenne muscular dystrophy (dmd) (2 trials)
1
Indication
--
Phase 3 Trials
1
Priority Reviews
9
Years on Market

Details

Status
Prescription
First Approved
2016-09-19
Patent Cliff
2034

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Routes
INTRAVENOUS
Dosage Forms
SOLUTION

Companies

Active Ingredient: ETEPLIRSEN

EXONDYS 51 Approval History

2017
2018
2019
2020
2021
2022
2023
2024
2025
2026
Original
New Indication
New Form
Label Update
18 FDA actions from 2016 to 2024
Dec 2024 SUPPL
Label · Labeling
Jan 2022 SUPPL
Label · Labeling
Jul 2020 SUPPL
Label · Labeling

What EXONDYS 51 Treats

1 indications

EXONDYS 51 is approved for 1 conditions since its original approval in 2016. These indications span multiple therapeutic areas including oncology, immunology, and more.

  • Duchenne Muscular Dystrophy
Source: FDA Label

EXONDYS 51 Competitive Set

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Filters applied: drops same-active-ingredient (505(b)(2) reformulations), route-mismatch (topical vs systemic), and cross-therapeutic-area matches in same-indication rings.

What's emerging in EXONDYS 51's indications

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Phase 3 candidates targeting molecules with no FDA-approved drug, in indications EXONDYS 51 treats. First-in-class if their pivotal trials read out positive.

Drugs Similar to EXONDYS 51

3 of 9

FDA-approved drugs for similar conditions. Compare mechanisms and indications to understand treatment alternatives.

AGAMREE
VAMOROLONE
1 shared
CATALYST PHARMS
Shared indications:
Duchenne Muscular Dystrophy
AMONDYS 45
CASIMERSEN
1 shared
Sarepta Therapeutics
Shared indications:
Duchenne Muscular Dystrophy
DEFLAZACORT
DEFLAZACORT
1 shared
ZYDUS LIFESCIENCES
Shared indications:
Duchenne Muscular Dystrophy
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Clinical Trial Registry

7 trials
Trial Sponsor ID Phase Status Title
NCT03992430 MIS51ON 4658-402 2018-001762-42, 2024-511492-15-00 Ph 3 active not recruiting A Study to Compare Safety and Efficacy of High Doses of Eteplirsen in Participants With Duchenne Muscular Dystrophy (DMD) (MIS51ON)
NCT04179409 results posted SRPT-Dup-US-001 Ph 2 completed A 48-Week, Open Label, Study to Evaluate the Efficacy and Safety of AMONDYS 45, EXONDYS 51, VYONDYS 53 in Subjects With DuchenneMuscular Dystrophy Carrying Eligible DMD Duplications.
NCT03985878 results posted 4658-102-OLE 2019-000337-39 Ph 2 terminated A Study to Evaluate Safety, Tolerability, and Efficacy of Eteplirsen in Participants With Duchenne Muscular Dystrophy (DMD) Who Have Completed Study 4658-102 (NCT03218995)
NCT03218995 results posted 4658-102 Ph 2 completed Study of Eteplirsen in Young Participants With Duchenne Muscular Dystrophy (DMD) Amenable to Exon 51 Skipping
NCT02420379 results posted 4658-203 Ph 2 completed Safety Study of Eteplirsen to Treat Early Stage Duchenne Muscular Dystrophy
NCT02255552 PROMOVI results posted 4658-301 Ph 3 completed Study of Eteplirsen in DMD Patients
NCT02286947 results posted 4658-204 Ph 2 completed Safety Study of Eteplirsen to Treat Advanced Stage Duchenne Muscular Dystrophy
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Active Pipeline

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Key Completed Trials

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Trial Timeline

Full development history with FDA approval milestones

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Understanding FDA Approval Types
Count Type What it means
- ORIG Original approval - drug first enters market
- SUPPL - Efficacy New indication (new disease/condition approved)
- SUPPL - Labeling Label text changes (warnings, dosing updates)
- SUPPL - Manufacturing Production changes (new facility)
- SUPPL - Chemistry Formulation changes (new dosage strength)

Green lines in the timeline show ORIG and Efficacy approvals - the clinically meaningful milestones.

EXONDYS 51 FDA Label Details

Indications & Usage

FDA Label (PDF)

EXONDYS 51 is indicated for the treatment of Duchenne Muscular Dystrophy.

View full patent landscape →
5 OB patents · 3 families · 151 international docs across 24 countries

EXONDYS 51 Patents & Exclusivity

Latest Patent: Mar 2034

Patents (5 active)

US9506058 Expires Mar 14, 2034
US10364431 Expires Mar 14, 2034
US10337003 Expires Mar 14, 2034
USRE47769 Expires Feb 2, 2029
USRE48468 Expires Oct 27, 2028
Source: FDA Orange Book

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Deep insights for EXONDYS 51

Revenue Insights

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  • Historical trend analysis

Patent Timeline

  • Cliff: 2034
  • 28 active patents

Trial Analysis

  • 7 total trials
  • Stage: Declining

Competitive Landscape

  • 9 similar drugs
  • Same target/indication analysis
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Data Sources

Data sourced from official FDA and NIH databases. Click links to verify on original sources.

How We Calculate These Metrics

Trial Activity Stage

Measures the current development activity pattern based on trial phases, status, and trends. Important: This measures R&D activity, not commercial lifecycle.

Trial statuses: "Active" means recruiting or ongoing. "Completed" means reached planned endpoint. "Terminated" means stopped early—often due to safety, efficacy, or business reasons.

  • Growth: High proportion of early-phase trials (Phase 1/2), active development
  • Expansion: Significant Phase 3 activity, approaching or pursuing approvals
  • Mature: Substantial Phase 4 post-marketing studies
  • Stable: Mixed phase distribution, steady development
  • Declining: Low active trial ratio, reduced R&D investment