TheraRadar
Data updated: May 26, 2026

SODIUM PHENYLBUTYRATE

Rare Disease Approved 2011-11-18

SODIUM PHENYLBUTYRATE is indicated for the treatment of Urea Cycle Disorder; Hyperammonemic Encephalopathy.

Source: FDA Label • NAVINTA LLC
6
Indications
--
Phase 3 Trials
14
Years on Market

Details

Status
Prescription
First Approved
2011-11-18
Routes
ORAL
Dosage Forms
TABLET, POWDER

SODIUM PHENYLBUTYRATE Approval History

2012
2013
2014
2015
2016
2017
2018
2019
2020
2021
2022
2023
2024
2025
2026
Original
New Indication
New Form
Label Update
6 FDA actions from 2011 to 2026
Feb 2026 ORIGINAL
Update
Nov 2022 ORIGINAL
Update
Jun 2016 ORIGINAL
Update

What SODIUM PHENYLBUTYRATE Treats

2 indications

SODIUM PHENYLBUTYRATE is approved for 2 conditions since its original approval in 2011. These indications span multiple therapeutic areas including oncology, immunology, and more.

  • Urea Cycle Disorder
  • Hyperammonemic Encephalopathy
Source: FDA Label

SODIUM PHENYLBUTYRATE Competitive Set

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Three rings of competition based on shared molecular targets and treated indications.

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Filters applied: drops same-active-ingredient (505(b)(2) reformulations), route-mismatch (topical vs systemic), and cross-therapeutic-area matches in same-indication rings.

Drugs Similar to SODIUM PHENYLBUTYRATE

3 of 4

FDA-approved drugs for similar conditions. Compare mechanisms and indications to understand treatment alternatives.

OLPRUVA
SODIUM PHENYLBUTYRATE
2 shared
ACER
Shared indications:
Urea Cycle DisorderHyperammonemic Encephalopathy
PHEBURANE
SODIUM PHENYLBUTYRATE
1 shared
MEDUNIK
Shared indications:
Urea Cycle Disorder
RAVICTI
GLYCEROL PHENYLBUTYRATE
1 shared
HORIZON THERAP US
Shared indications:
Urea Cycle Disorder
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Clinical Trial Registry

9 trials
Trial Sponsor ID Phase Status Title
NCT06069375 STUDY23060034 Ph 2 suspended Study of Sodium Phenylbutyrate (ACER-001) for the Treatment of Patients With Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCADD)
NCT07125066 STUDY25060137 Ph 1 enrolling by invitation An Individual Patient, Open Label Study to Use ACER-001 to Treat Combined D,L-2 Hydroxyglutaric Aciduria (C-2HGA)
NCT06773026 STUDY24100064 Ph 2 recruiting Study of Sodium Phenylbutyrate (ACER-001) for the Treatment of Pediatric and Adults Patients With Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCADD)
NCT05349435 PBI-4050-CT-9-21 Ph 1 terminated A Healthy Volunteer Study to Compare Fezagepras (PBI-4050) With Sodium Phenylbutyrate
NCT03734263 TIGEM2-PDH TIGEM2-PDH Ph 2 completed Use of Phenylbutyrate Therapy for Patients With Pyruvate Dehydrogenase Complex Deficiency.
NCT00345605 results posted RDCRN 5102 U54HD061221 Ph 2 completed Arginine and Buphenyl in Patients With Argininosuccinic Aciduria (ASA), a Urea Cycle Disorder
NCT01096095 CONEP CAAE 0527.0.001.000-07 Ph 2 withdrawn Pilot Study of Safety and Efficacy of Sodium Phenylbutyrate in Spinocerebellar Ataxia Type 3
NCT00439218 NPTUNE 02 results posted N01NS42361_NPTUNE02 HHSN265200423611C, N01NS42361 Ph 1, Ph 2 terminated Clinical Trial of Sodium Phenylbutyrate in Children With Spinal Muscular Atrophy Type I
NCT00439569 NPTUNE01 results posted N01NS42361_NPTUNE01 HHSN265200423611C, N01NS42361 Ph 1, Ph 2 terminated Clinical Trial of Sodium Phenylbutyrate in Children With Spinal Muscular Atrophy Types II or III
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Active Pipeline

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Ongoing clinical trials by development phase

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Key Completed Trials

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Completed studies with published results, ranked by significance

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Trial Timeline

Full development history with FDA approval milestones

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Understanding FDA Approval Types
Count Type What it means
- ORIG Original approval - drug first enters market
- SUPPL - Efficacy New indication (new disease/condition approved)
- SUPPL - Labeling Label text changes (warnings, dosing updates)
- SUPPL - Manufacturing Production changes (new facility)
- SUPPL - Chemistry Formulation changes (new dosage strength)

Green lines in the timeline show ORIG and Efficacy approvals - the clinically meaningful milestones.

SODIUM PHENYLBUTYRATE FDA Label Details

Indications & Usage

SODIUM PHENYLBUTYRATE is indicated for the treatment of Urea Cycle Disorder; Hyperammonemic Encephalopathy.

Looking for the branded version?

OLPRUVA

Full clinical data, patents, trials, and competitive landscape for sodium phenylbutyrate.

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Data Sources

Data sourced from official FDA and NIH databases. Click links to verify on original sources.